All evaluations median (IQR) | Classic DYS (n = 22) | Classic nDYS (n = 55) | Classic DYS vs. nDYS* | Strain DYS (n = 44) | Strain nDYS (n = 33) | Strain DYS vs. nDYS* | Classic DYS vs. strain DYS* |
---|---|---|---|---|---|---|---|
LVEF (%) | 55.08 (40.40–63.08) | 51.93 (45.02–60.04) | n.s | 51.98 (41.40–60.49) | 52.67 (47.32–61.64) | n.s | n.s |
LV GLS (%) | 24.66 (20.85–30.19) | 24.06 (20.28–27.80) | n.s | 23.72 (18.71–29.00) | 25.16 (21.63–28.00) | n.s | n.s |
MAPSE (mm) | 16.50 (14.70–17.98) | 16.20 (15.00–17.80) | n.s | 16.05 (14.93–18.25) | 16.30 (15.00–17.80) | n.s | n.s |
LA-ƐCT (%) | 9.66 (6.65–13.23) | 11.10 (6.20–15.23) | n.s | 6.75 (4.63–9.74) | 14.50 (12.69–18.63) | < 0.0001 | 0.0577 |
LA-Ɛ (%) | 26.35 (21.13–29.07) | 30.00 (19.80–38.42) | 0.0582 | 22.15 (17.80–27.30) | 37.50 (33.25–42.01) | < 0.0001 | 0.0403 |
LV A (cm/s) | 78.20 (57.95–90.75) | 63.45 (55.78–81.98) | n.s | 66.35 (55.40–82.25) | 64.20 (57.55–93.65) | n.s | n.s |
LV E (cm/s) | 59.00 (53.75–78.30) | 73.10 (63.20–84.60) | 0.0041 | 67.85 (57.45–79.65) | 71.50 (60.25–83.30) | n.s | n.s |
LV E/A | 0.74 (0.62–1.08) | 1.08 (0.89–1.33) | 0.0005 | 0.97 (0.76–1.36) | 1.03 (0.82–1.29) | n.s | 0.0288 |
LV e' lat (cm/s) | 9.65 (7.15–10.78) | 10.80 (9.20–12.80) | 0.0114 | 10.45 (8.13–12.80) | 9.80 (9.00–11.45) | n.s | n.s |
LV e' sep (cm/s) | 6.60 (5.80–8.10) | 8.50 (7.00–10.10) | 0.0087 | 7.78 (6.50–11.50) | 7.90 (6.50–9.20) | n.s | n.s |
LV E/e' | 7.62 (5.91–9.39) | 7.63 (6.72–9.15) | n.s | 7.58 (6.24–9.27) | 7.80 (6.81–9.20) | n.s | n.s |
LV IVCT (msec) | 67.00 (51.00–79.00) | 85.00 (71.00–103.50) | n.s | 70.00 (51.00–79.00) | 50.00 (42.00–64.00) | 0.0018 | n.s |
LV pre-ET (msec) | 71.50 (56.00–81.25) | 71.00 (54.00–88.00) | n.s | 74.00 (67.00–88.00) | 63.00 (42.50–81.00) | 0.0297 | n.s |
RV FAC (%) | 42.34 (31.21–51.15) | 43.03 (40.13–52.28) | n.s | 41.51 (33.59–48.03) | 48.61 (40.96–58.32) | 0.0022 | n.s |
RV GLS (%) | 25.99 (19.11–34.27) | 24.03 (18.89–29.22) | n.s | 21.85 (18.50–29.24) | 26.95 (22.38–31.59) | 0.0303 | n.s |
TAPSE (mm) | 21.10 (18.88–23.35) | 22.30 (20.50–25.00) | n.s | 21.55 (19.45–23.35) | 22.80 (20.60–25.10) | n.s | n.s |
RV S' (cm/s) | 14.90 (13.25–16.28) | 15.90 (12.40–18.00) | n.s | 14.90 (12.65–17.45) | 15.80 (12.50–17.60) | n.s | n.s |
RV e' (cm/s) | 9.40 (6.68–13.43) | 10.20 (8.00–14.40) | n.s | 11.25 (8.70–14.98) | 9.50 (7.65–12.70) | 0.0331 | n.s |
CI (l/min/m2) | 2.47 (1.99–3.42) | 2.67 (2.20–3.04) | n.s | 2.47 (2.01–2.92) | 2.83 (2.24–4.11) | 0.0473 | n.s |
NTproBNP (pg/ml) | 275.00 (95.30–643.80) | 214.00 (84.00–923.00) | n.s | 229.50 (79.05–1016.00) | 262.00 (107.00–650.00) | n.s | n.s |
Troponin (ng/l) | 13.00 (13.00–15.17) | 13.00 (13–23.70) | n.s | 13.00 (13.00–16.55) | 13.10 (13.00–20.14) | n.s | n.s |